Deafness with vestibular dysfunction (DINGS1), is a neurological disorder caused by poor development of the inner ear. This includes the cochlea (the part of the inner ear that produces nerve impulses in response to sound vibrations) as well as the vestibular labyrinth (interconnected canals of the inner ear assisting with balance, as well other functions). In affected dogs, the lack of proper development of the cochlea prevents sounds being sent from the ear to the brain. The vestibular labyrinth, which is directly connected to the cochlea, provides information regarding motion, spatial orientation, and head position to the brain. There is no treatment for this disorder.
Signs begin developing in puppies and worsen with age. An affected dog may have vertigo, dizziness, balance issues as well as spatial orientation issues. Symptoms can present as mild to severe but are early onset and can be progressive.
DNA testing is available to identify clear, carrier and affected dogs. A BAER hearing test from your veterinarian can also provide more information as to the degree of deafness and vestibular impact.
Gene Tested : PTPRQ